Carnitine
Name: Vitamin BT; β-hydroxy-γ-N-trimethylaminobutyric acid, 3-hydroxy-4-N,N,N- trimethylaminobutyrate.
Chemistry: quaternary ammonium compound; involved in metabolism in most mammals, plants and some bacteria. Carnitine has two isomers, labeled D-carnitine and L-carnitine; at room temperature carnitine is a white powder, and a water-soluble zwitterion with low toxicity; Carnitine is involved in the oxidation of fatty acids, and involved in systemic primary carnitine deficiency